Hepatic trisegmentectomy hepatoblastoma in a 3-year-old patient

Abstract

Introduction: liver cancer in children, mainly hepatoblastoma, is uncommon, but accounts for approximately 1-2% of all childhood cancers. Although it is the most common primary liver cancer in children, its five-year survival rate is low due to resistance to chemotherapy in 20% of cases. The annual incidence in children under 1 year is 11.2 cases per million. Hepatoblastoma tends to affect white children more and is more common in boys than in girls, especially before the age of 5.

Clinical case: a female patient with an upper respiratory condition, with no significant history, whose physical examination detects hepatomegaly without other accompanying symptoms, it is decided to perform complementary examinations to reach the diagnosis.

Evolution: patient with hepatomegaly, laboratory tests are performed, and abdominal ultrasound shows rounded formations in liver without vascularization. A diagnostic laparoscopy was performed, and a solid tumor mass was removed from segment IV of the liver and the sickle ligament. Histopathological analyses revealed hepatoblastoma fetal Follow-up examinations showed decrease of tumor markers and postoperative changes in the surgical bed.

Conclusion: initial surgery in children with stage I hepatoblastoma is considered safe and feasible, without chemotherapy needed. And avoid its side effects. When the tumors are completely resected, there is a possibility of long-term survival without the need for chemotherapy.

Keywords

Hepatoblastoma (HB), PRETEXT I, Hepatectomy, Trisegmentectomy

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